Extrapyramidal involvement in Rett’s syndrome

Academic Article


  • Extrapyramidal dysfunction is poorly characterized in Rett’s syndrome, a neurodegenerative disorder in girls. We studied the motor and behavioral findings in 32 Ftett’s syndrome patients, 21 months to 30 years old. In addition to the typical stereotyped movements and scoliosis, other motor disturbances included bruxism, sialorrhea, ocular deviations, parkinsonian findings, dystonia, myoclonus, and athetosis. The types of movement disorders seemed to be age-related, with the hyperkinetic disorders occurring in the younger patients and the bradykinetic disorders occurring more frequently in the older patients. © 1990 American Academy of Neurology.
  • Authors

    Published In

  • Neurology  Journal
  • Digital Object Identifier (doi)

    Author List

  • FitzGerald PM; Jankovic J; Glaze DG; Schultz R; Percy AK
  • Start Page

  • 293
  • End Page

  • 295
  • Volume

  • 40
  • Issue

  • 2