The congenital porto-caval fistula: A unique presentation and novel intervention

Academic Article


  • Congenital porto-caval tistulas are uncommon vascular malformations with a varied clinical presentation beginning in intancy and spanning late adulthood. We report a 14-year-old male who presented with dyspnea and cough. His past medical history was signiticant tor a chronic non-immune hemolytic anemia, thrombocytopenia, coagulopathy and a learning disability. He was found to have severe pulmonary hypertension and hyperammonemia associated with a large congenital porto-caval tistula. The abnormal vessel was occluded via endovascular covered stent placement in the vena cava. His pulmonary hypertension has improved remarkably while his chronic anemia, thrombocytopenia and ammonia have normalized to allow improved cognitive performance. © 2007 Wiley-Liss, Inc.
  • Authors

    Published In

    Digital Object Identifier (doi)

    Author List

  • Hoover W; Ackerman V; Schamberger M; Kumar M; Marshalleck F; Hoyer M
  • Start Page

  • 196
  • End Page

  • 199
  • Volume

  • 43
  • Issue

  • 2