Desmoplastic fibroma of bone is an exceedingly rare tumor that was first described by Jaffe in 1958 . It has a high incidence of local recurrence after surgical resection. It is usually seen in young patients and involves mandible and long bones. It has histological resemblance to the desmoid tumor of the abdominal wall. We report a surgically proven case of desmoplastic fibroma of bone with local aggressiveness and recurrence during follow-up. The radiograph, CT imaging features, radiological and pathological differential diagnosis of the case are described, and literature is briefly reviewed. © 2003 Elsevier Science Inc. All rights reserved.