Introduction: Jugular paragangliomas are rare neuroendocrine tumours of the lateral skull base, comprising only 0.6% of all head and neck tumours. Their indolent nature together with their deep seated anatomical location can result in delayed presentation. The challenge in management lies in determining the risk/benefit ratio of treatment as surgery is frequently associated with high morbidity in a disease with an overall low mortality. This paper includes a thorough review of the current literature reviewing epidemiology, presentation, investigation and treatment.
