Signet ring cell carcinoma (SRCC) is a subtype of adenocarcinoma. It can arise in different organs including stomach, colon, bladder, prostate and breast. The vast majority of SRCC found in the pulmonary system is metastatic. Primary disease to the lungs is rare. The main feature of this type of malignancy is mucinproducing cells. It has been reported that out of 3500 cases of pulmonary adenocarcinoma, five cases had features of SRCC. © the authors; licensee ecancermedicalscience.