Positions

Selected Publications

Academic Article

Year Title Altmetric
2022 Ivacaftor-elexacaftor-tezacaftor and tacrolimus combination in cystic fibrosis.  Journal of Cystic Fibrosis.  21:e8-e10. 2022
2022 Use of elexacaftor/tezacaftor/ivacaftor among cystic fibrosis lung transplant recipients.  Journal of Cystic Fibrosis.  2022
2021 CFTR function and clinical response to modulators parallel nasal epithelial organoid swelling 2021
2021 Combination CFTR modulator therapy in children and adults with cystic fibrosis 2021
2021 Long term clinical effectiveness of ivacaftor in people with the G551D CFTR mutation.  Journal of Cystic Fibrosis.  20:213-219. 2021
2020 Highlights from the 2019 North American Cystic Fibrosis Conference.  Pediatric Pulmonology.  55:2225-2232. 2020
2020 Variable cellular ivacaftor concentrations in people with cystic fibrosis on modulator therapy.  Journal of Cystic Fibrosis.  19:742-745. 2020
2020 Human nasal epithelial organoids for therapeutic development in cystic fibrosis.  Genes.  11:1-17. 2020
2020 Females with cystic fibrosis demonstrate a differential response profile to ivacaftor compared with males.  American Journal of Respiratory and Critical Care Medicine.  201:996-998. 2020
2019 Co-cultured microfluidic model of the airway optimized for microscopy and micro-optical coherence tomography imaging.  Biomedical Optics Express.  10:5414-5430. 2019
2019 Effectiveness of ivacaftor in cystic fibrosis patients with non-G551D gating mutations.  Journal of Cystic Fibrosis.  18:102-109. 2019
2018 Tracheostomy in children: Epidemiology and clinical outcomes.  Pediatric Pulmonology.  53:1269-1275. 2018
2018 Potential pathogenicity of Inquilinus limosus in a pediatric patient with cystic fibrosis.  Pediatric Pulmonology.  53:E21-E23. 2018
2018 Sensitivity of ivacaftor to drug-drug interactions with rifampin, a cytochrome P450 3A4 inducer.  Pediatric pulmonology. Supplement.  53:E6-E8. 2018
2017 Nasospheroids permit measurements of CFTR-dependent fluid transport.  JCI Insight.  2. 2017
2017 Toward inclusive therapy with CFTR modulators: Progress and challenges.  Pediatric pulmonology. Supplement.  52:S4-S14. 2017
2009 Correlation of microRNA levels during hypoxia with predicted target mRNAs through genome-wide microarray analysis.  BMC Medical Genomics.  2. 2009
2008 Role of oxygen availability in CFTR expression and function.  American Journal of Respiratory Cell and Molecular Biology.  39:514-521. 2008
2004 Efficient intracellular processing of the endogenous cystic fibrosis transmembrane conductance regulator in epithelial cell lines.  Journal of Biological Chemistry.  279:22578-22584. 2004
2003 EWS/FLI function varies in different cellular backgrounds.  Experimental Cell Research.  290:414-419. 2003
2001 Peptides, made to order.  Scientist (Philadelphia, Pa.).  15:25-26. 2001
2001 Tailored arrays.  Scientist (Philadelphia, Pa.).  15:26-28. 2001

Principal Investigator On

Investigator On

Full Name

  • Jennifer Guimbellot