Year |
Title |
Altmetric |
2019
|
Herbal dry extract BNO 1011 improves clinical and mucociliary parameters in a rabbit model of chronic rhinosinusitis..
International Forum of Allergy and Rhinology.
2019
|
|
2019
|
Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction and Radiographic Bronchiectasis in Current and Former Smokers: A Cross-Sectional Study..
Annals of the American Thoracic Society.
16:150-153.
2019
|
|
2019
|
CFTR modulator theratyping: Current status, gaps and future directions..
Journal of Cystic Fibrosis.
18:22-34.
2019
|
|
2019
|
Effectiveness of ivacaftor in cystic fibrosis patients with non-G551D gating mutations..
Journal of Cystic Fibrosis.
18:102-109.
2019
|
|
2018
|
Vaporized E-Cigarette Liquids Induce Ion Transport Dysfunction in Airway Epithelia..
American Journal of Respiratory Cell and Molecular Biology.
2018
|
|
2018
|
Effect of ivacaftor on mucociliary clearance and clinical outcomes in cystic fibrosis patients with G551D-CFTR..
JCI insight.
3.
2018
|
|
2018
|
Muc5b overexpression causes mucociliary dysfunction and enhances lung fibrosis in mice..
Nature Communications.
9:5363.
2018
|
|
2018
|
Objective Versus Self-Reported Adherence to Airway Clearance Therapy in Cystic Fibrosis..
Respiratory Care.
2018
|
|
2018
|
The epithelial sodium channel (ENaC) as a therapeutic target for cystic fibrosis..
Current Opinion in Pharmacology.
43:152-165.
2018
|
|
2018
|
Colocolonic intussusception in an adult cystic fibrosis patient..
Journal of Cystic Fibrosis.
2018
|
|
2018
|
Antisense oligonucleotide eluforsen improves CFTR function in F508del cystic fibrosis..
Journal of Cystic Fibrosis.
2018
|
|
2018
|
Heme scavenging reduces pulmonary endoplasmic reticulum stress, fibrosis, and emphysema..
JCI insight.
3.
2018
|
|
2018
|
Functional Anatomic Imaging of the Airway Surface..
Annals of the American Thoracic Society.
15:S177-S183.
2018
|
|
2018
|
Non-obstructive vas deferens and epididymis loss in cystic fibrosis rats..
Mechanisms of Development.
2018
|
|
2018
|
Influenza-mediated reduction of lung epithelial ion channel activity leads to dysregulated pulmonary fluid homeostasis..
JCI insight.
3.
2018
|
|
2018
|
VX-445-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles..
New England Journal of Medicine.
379:1612-1620.
2018
|
|
2018
|
VX-659-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles..
New England Journal of Medicine.
379:1599-1611.
2018
|
|
2018
|
Ataluren, a New Therapeutic for Alpha-1 Antitrypsin-Deficient Individuals with Nonsense Mutations..
American Journal of Respiratory and Critical Care Medicine.
198:1099-1102.
2018
|
|
2018
|
Standardized Measurement of Nasal Membrane Transepithelial Potential Difference (NPD)..
Journal of Visualized Experiments.
2018
|
|
2018
|
EMPIRE-CF: A phase II randomized placebo-controlled trial of once-daily, oral acebilustat in adult patients with cystic fibrosis - Study design and patient demographics..
Controlled Clinical Trials.
72:86-94.
2018
|
|
2018
|
Changes in Lung Clearance Index in Preschool-aged Patients with Cystic Fibrosis Treated with Ivacaftor (GOAL): A Clinical Trial..
American Journal of Respiratory and Critical Care Medicine.
198:526-528.
2018
|
|
2018
|
A revised airway epithelial hierarchy includes CFTR-expressing ionocytes..
Nature.
560:319-324.
2018
|
|
2018
|
Maternal Smoking Induces Acquired CFTR Dysfunction in Neonatal Rats..
American Journal of Respiratory and Critical Care Medicine.
198:672-674.
2018
|
|
2018
|
An Adeno-Associated Viral Vector Capable of Penetrating the Mucus Barrier to Inhaled Gene Therapy..
Molecular Therapy - Methods and Clinical Development.
9:296-304.
2018
|
|
2018
|
Ivacaftor-treated Patients with Cystic Fibrosis Derive Long-Term Benefit Despite No Short-Term Clinical Improvement..
American Journal of Respiratory and Critical Care Medicine.
197:1483-1486.
2018
|
|
2018
|
Seeing cilia: imaging modalities for ciliary motion and clinical connections..
AJP - Lung Cellular and Molecular Physiology.
314:L909-L921.
2018
|
|
2018
|
Sensitivity of ivacaftor to drug-drug interactions with rifampin, a cytochrome P450 3A4 inducer..
Pediatric Pulmonology.
53:E6-E8.
2018
|
|
2018
|
MicroRNA-145 Antagonism Reverses TGF-β Inhibition of F508del CFTR Correction in Airway Epithelia..
American Journal of Respiratory and Critical Care Medicine.
197:632-643.
2018
|
|
2018
|
Implementation of a successful eradication protocol for Burkholderia Cepacia complex in cystic fibrosis patients..
BMC Pulmonary Medicine.
18:35.
2018
|
|
2018
|
Development of an airway mucus defect in the cystic fibrosis rat..
JCI insight.
3.
2018
|
|
2017
|
Not simply the lesser of two evils..
AJP - Lung Cellular and Molecular Physiology.
314:L236-L238.
2017
|
|
2017
|
The therapeutic potential of CFTR modulators for COPD and other airway diseases..
Current Opinion in Pharmacology.
34:132-139.
2017
|
|
2017
|
Tezacaftor-Ivacaftor in Residual-Function Heterozygotes with Cystic Fibrosis..
New England Journal of Medicine.
377:2024-2035.
2017
|
|
2017
|
Toward inclusive therapy with CFTR modulators: Progress and challenges..
Pediatric Pulmonology.
52:S4-S14.
2017
|
|
2017
|
Klotho Inhibits Interleukin-8 Secretion from Cystic Fibrosis Airway Epithelia..
Scientific Reports.
7:14388.
2017
|
|
2017
|
Roflumilast reverses CFTR-mediated ion transport dysfunction in cigarette smoke-exposed mice..
Respiratory Research.
18:173.
2017
|
|
2017
|
A multiple reader scoring system for Nasal Potential Difference parameters..
Journal of Cystic Fibrosis.
16:573-578.
2017
|
|
2017
|
Identification of the amino acids inserted during suppression of CFTR nonsense mutations and determination of their functional consequences..
Human Molecular Genetics.
26:3116-3129.
2017
|
|
2017
|
Impact of CFTR Modulation on Intestinal pH, Motility, and Clinical Outcomes in Patients With Cystic Fibrosis and the G551D Mutation..
Clinical and Translational Gastroenterology.
8:e81.
2017
|
|
2017
|
Assessment of ciliary phenotype in primary ciliary dyskinesia by micro-optical coherence tomography..
JCI insight.
2:e91702.
2017
|
|
2017
|
Protective and antifungal properties of Nanodisk-Amphotericin B over commercially available Amphotericin B..
World Journal of Otorhinolaryngology-Head and Neck Surgery.
3:2-8.
2017
|
|
2017
|
Flexible, high-resolution micro-optical coherence tomography endobronchial probe toward in vivo imaging of cilia..
Optics Letters.
42:867-870.
2017
|
|
2017
|
Growth in Prepubertal Children With Cystic Fibrosis Treated With Ivacaftor..
Pediatrics.
139.
2017
|
|
2017
|
Lumacaftor/Ivacaftor Treatment of Patients with Cystic Fibrosis Heterozygous for F508del-CFTR..
Annals of the American Thoracic Society.
14:213-219.
2017
|
|
2017
|
A Case Report of Pregnancy During Use of Targeted Therapeutics for Cystic Fibrosis..
JOGN nursing; journal of obstetric, gynecologic, and neonatal nursing.
46:72-77.
2017
|
|
2017
|
Applying recent advances in the science of CFTR-based therapeutics to improve outcomes in patients with cystic fibrosis.
Journal of Cystic Fibrosis.
2017
|
|
2017
|
Assessment of acquired mucociliary clearance defects using micro-optical coherence tomography..
International Forum of Allergy and Rhinology.
7:920-925.
2017
|
|
2017
|
Reduced bone length, growth plate thickness, bone content, and IGF-I as a model for poor growth in the CFTR-deficient rat..
PLoS ONE.
12:e0188497.
2017
|
|
2017
|
Sinus Microanatomy and Microbiota in a Rabbit Model of Rhinosinusitis..
Frontiers in Cellular and Infection Microbiology.
7:540.
2017
|
|
2017
|
Use of ferrets for electrophysiologic monitoring of ion transport..
PLoS ONE.
12:e0186984.
2017
|
|
2016
|
A little CFTR can change a lot: slowing cystic fibrosis progression..
Lancet Respiratory Medicine.
5:86-87.
2016
|
|
2016
|
Ataluren stimulates ribosomal selection of near-cognate tRNAs to promote nonsense suppression..
Proceedings of the National Academy of Sciences.
113:12508-12513.
2016
|
|
2016
|
Therapeutic benefit observed with the CFTR potentiator, ivacaftor, in a CF patient homozygous for the W1282X CFTR nonsense mutation..
Journal of Cystic Fibrosis.
16:24-29.
2016
|
|
2016
|
A ferret model of COPD-related chronic bronchitis..
JCI insight.
1:e87536.
2016
|
|
2016
|
Particle-Tracking Microrheology Using Micro-Optical Coherence Tomography..
Biophysical Journal.
111:1053-1063.
2016
|
|
2016
|
The Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor Augments Mucociliary Clearance Abrogating Cystic Fibrosis Transmembrane Conductance Regulator Inhibition by Cigarette Smoke..
American Journal of Respiratory Cell and Molecular Biology.
56:99-108.
2016
|
|
2016
|
Dual SMAD Signaling Inhibition Enables Long-Term Expansion of Diverse Epithelial Basal Cells..
Cell Stem Cell.
19:217-231.
2016
|
|
2016
|
In vivo imaging of airway cilia and mucus clearance with micro-optical coherence tomography..
Biomedical Optics Express.
7:2494-2505.
2016
|
|
2016
|
Mutation of Growth Arrest Specific 8 Reveals a Role in Motile Cilia Function and Human Disease..
PLoS Genetics.
12:e1006220.
2016
|
|
2016
|
Pulmonary artery enlargement and cystic fibrosis pulmonary exacerbations: a cohort study..
Lancet Respiratory Medicine.
4:636-645.
2016
|
|
2016
|
Pilot evaluation of ivacaftor for chronic bronchitis..
Lancet Respiratory Medicine.
4:e32-e33.
2016
|
|
2016
|
Discovery of Clinically Approved Agents That Promote Suppression of Cystic Fibrosis Transmembrane Conductance Regulator Nonsense Mutations..
American Journal of Respiratory and Critical Care Medicine.
194:1092-1103.
2016
|
|
2016
|
Therapeutic Approaches to Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in Chronic Bronchitis..
Annals of the American Thoracic Society.
13 Suppl 2:S169-S176.
2016
|
|
2016
|
New and emerging targeted therapies for cystic fibrosis..
BMJ.
352:i859.
2016
|
|
2016
|
Combination therapy with cystic fibrosis transmembrane conductance regulator modulators augment the airway functional microanatomy..
AJP - Lung Cellular and Molecular Physiology.
310:L928-L939.
2016
|
|
2016
|
Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in Chronic Bronchitis and Other Diseases of Mucus Clearance..
Clinics in Chest Medicine.
37:147-158.
2016
|
|
2016
|
Alterations in blood leukocytes of G551D-bearing cystic fibrosis patients undergoing treatment with ivacaftor..
Journal of Cystic Fibrosis.
15:67-73.
2016
|
|
2016
|
Codon bias and the folding dynamics of the cystic fibrosis transmembrane conductance regulator..
Cellular and Molecular Biology Letters.
21:23.
2016
|
|
2016
|
Increasing the Endoplasmic Reticulum Pool of the F508del Allele of the Cystic Fibrosis Transmembrane Conductance Regulator Leads to Greater Folding Correction by Small Molecule Therapeutics..
PLoS ONE.
11:e0163615.
2016
|
|
2015
|
Recovery of Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction after Smoking Cessation..
American Journal of Respiratory and Critical Care Medicine.
192:1521-1524.
2015
|
|
2015
|
Breakthrough therapies: Cystic fibrosis (CF) potentiators and correctors..
Pediatric Pulmonology.
50 Suppl 40:S3-S13.
2015
|
|
2015
|
Heme oxygenase-1-mediated autophagy protects against pulmonary endothelial cell death and development of emphysema in cadmium-treated mice..
AJP - Lung Cellular and Molecular Physiology.
309:L280-L292.
2015
|
|
2015
|
Moderate intensity exercise mediates comparable increases in exhaled chloride as albuterol in individuals with cystic fibrosis..
Respiratory Medicine.
109:1001-1011.
2015
|
|
2015
|
Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR..
New England Journal of Medicine.
373:220-231.
2015
|
|
2015
|
Efficacy and safety of ivacaftor in patients with cystic fibrosis who have an Arg117His-CFTR mutation: a double-blind, randomised controlled trial..
Lancet Respiratory Medicine.
3:524-533.
2015
|
|
2015
|
Defective innate immunity and hyperinflammation in newborn cystic fibrosis transmembrane conductance regulator-knockout ferret lungs..
American Journal of Respiratory Cell and Molecular Biology.
52:683-694.
2015
|
|
2015
|
Improved clinical and radiographic outcomes after treatment with ivacaftor in a young adult with cystic fibrosis with the P67L CFTR mutation..
Chest.
147:e79-e82.
2015
|
|
2015
|
Novel outcome measures for clinical trials in cystic fibrosis..
Pediatric Pulmonology.
50:302-315.
2015
|
|
2015
|
Pseudomonas aeruginosa in cystic fibrosis patients with G551D-CFTR treated with ivacaftor..
Clinical Infectious Diseases.
60:703-712.
2015
|
|
2015
|
Cystic fibrosis..
Nature Reviews Disease Primers.
1:15010.
2015
|
|
2015
|
ΔF508 CFTR surface stability is regulated by DAB2 and CHIP-mediated ubiquitination in post-endocytic compartments..
PLoS ONE.
10:e0123131.
2015
|
|
2014
|
An autoregulatory mechanism governing mucociliary transport is sensitive to mucus load..
American Journal of Respiratory Cell and Molecular Biology.
51:485-493.
2014
|
|
2014
|
A functional anatomic defect of the cystic fibrosis airway..
American Journal of Respiratory and Critical Care Medicine.
190:421-432.
2014
|
|
2014
|
Development and maintenance of a biospecimen repository for clinical samples derived from pulmonary patients..
Clinical and Translational Science.
7:336-341.
2014
|
|
2014
|
Overcoming the cystic fibrosis sputum barrier to leading adeno-associated virus gene therapy vectors..
Molecular Therapy.
22:1484-1493.
2014
|
|
2014
|
Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosis..
American Journal of Respiratory and Critical Care Medicine.
190:175-184.
2014
|
|
2014
|
A CFTR corrector (lumacaftor) and a CFTR potentiator (ivacaftor) for treatment of patients with cystic fibrosis who have a phe508del CFTR mutation: a phase 2 randomised controlled trial..
Lancet Respiratory Medicine.
2:527-538.
2014
|
|
2014
|
Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial..
Lancet Respiratory Medicine.
2:539-547.
2014
|
|
2014
|
Porcine nasal epithelial cultures for studies of cystic fibrosis sinusitis..
International Forum of Allergy and Rhinology.
4:565-570.
2014
|
|
2014
|
The unfolded protein response affects readthrough of premature termination codons..
EMBO Molecular Medicine.
6:685-701.
2014
|
|
2014
|
Synthetic aminoglycosides efficiently suppress cystic fibrosis transmembrane conductance regulator nonsense mutations and are enhanced by ivacaftor..
American Journal of Respiratory Cell and Molecular Biology.
50:805-816.
2014
|
|
2014
|
Cystic fibrosis transmembrane conductance regulator activation by roflumilast contributes to therapeutic benefit in chronic bronchitis..
American Journal of Respiratory Cell and Molecular Biology.
50:549-558.
2014
|
|
2014
|
Sweat chloride as a biomarker of CFTR activity: proof of concept and ivacaftor clinical trial data..
Journal of Cystic Fibrosis.
13:139-147.
2014
|
|
2014
|
Acquired defects in CFTR-dependent β-adrenergic sweat secretion in chronic obstructive pulmonary disease..
Respiratory Research.
15:25.
2014
|
|
2014
|
Impact of heterozygote CFTR mutations in COPD patients with chronic bronchitis..
Respiratory Research.
15:18.
2014
|
|
2014
|
Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats..
PLoS ONE.
9:e91253.
2014
|
|
2014
|
Evaluating the predictive ability of sweat chloride..
Journal of Cystic Fibrosis.
13:118.
2014
|
|
2013
|
Cigarette smoke induces systemic defects in cystic fibrosis transmembrane conductance regulator function.
American Journal of Respiratory and Critical Care Medicine.
188:1321-1330.
2013
|
|
2013
|
Cigarette smoke induces systemic defects in cystic fibrosis transmembrane conductance regulator function..
American Journal of Respiratory and Critical Care Medicine.
188:1321-1330.
2013
|
|
2013
|
Cigarette smoke and CFTR: implications in the pathogenesis of COPD..
AJP - Lung Cellular and Molecular Physiology.
305:L530-L541.
2013
|
|
2013
|
Understanding the relationship between sweat chloride and lung function in cystic fibrosis..
Chest.
144:1418.
2013
|
|
2013
|
Cystic fibrosis chronic rhinosinusitis: a comprehensive review..
American Journal of Rhinology.
27:387-395.
2013
|
|
2013
|
Acquired cystic fibrosis transmembrane conductance regulator dysfunction in the lower airways in COPD..
Chest.
144:498-506.
2013
|
|
2013
|
Comparison of cystic fibrosis transmembrane conductance regulator (CFTR) and ciliary beat frequency activation by the CFTR Modulators Genistein, VRT-532, and UCCF-152 in primary sinonasal epithelial cultures..
JAMA Otolaryngology-Head and Neck Surgery.
139:822-827.
2013
|
|
2013
|
Cystic fibrosis transmembrane regulator correctors and potentiators.
Cold Spring Harbor perspectives in biology.
5.
2013
|
|
2013
|
Cystic fibrosis transmembrane regulator correctors and potentiators.
Cold Spring Harbor perspectives in biology.
5.
2013
|
|
2013
|
Cystic fibrosis transmembrane regulator correctors and potentiators..
Cold Spring Harbor perspectives in medicine.
3.
2013
|
|
2013
|
Reduced sodium transport with nasal administration of the prostasin inhibitor camostat in subjects with cystic fibrosis..
Chest.
144:200-207.
2013
|
|
2013
|
CFTR biomarkers: time for promotion to surrogate end-point..
European Respiratory Journal.
41:203-216.
2013
|
|
2013
|
IP-10 is a potential biomarker of cystic fibrosis acute pulmonary exacerbations..
PLoS ONE.
8:e72398.
2013
|
|
2013
|
Method for quantitative study of airway functional microanatomy using micro-optical coherence tomography..
PLoS ONE.
8:e54473.
2013
|
|
2013
|
Multicenter intestinal current measurements in rectal biopsies from CF and non-CF subjects to monitor CFTR function..
PLoS ONE.
8:e73905.
2013
|
|
2013
|
Optimizing nasal potential difference analysis for CFTR modulator development: assessment of ivacaftor in CF subjects with the G551D-CFTR mutation..
PLoS ONE.
8:e66955.
2013
|
|
2012
|
Clearance of initial mucoid Pseudomonas aeruginosa in patients with cystic fibrosis..
Pediatric Pulmonology.
47:1113-1122.
2012
|
|
2012
|
Progress in cystic fibrosis and the CF Therapeutics Development Network..
Thorax.
67:882-890.
2012
|
|
2012
|
Dab2 is a key regulator of endocytosis and post-endocytic trafficking of the cystic fibrosis transmembrane conductance regulator..
Biochemical Journal.
441:633-643.
2012
|
|
2012
|
A pharmacologic approach to acquired cystic fibrosis transmembrane conductance regulator dysfunction in smoking related lung disease..
PLoS ONE.
7:e39809.
2012
|
|
2012
|
CFTR potentiator treatment of cystic fibrosis.
Drugs of the future.
37:167-174.
2012
|
|
2012
|
Extensive surgical and comprehensive postoperative medical management for cystic fibrosis chronic rhinosinusitis..
American Journal of Rhinology.
26:70-75.
2012
|
|
2012
|
Purification of CFTR for mass spectrometry analysis: identification of palmitoylation and other post-translational modifications..
Protein Engineering -Oxford-.
25:7-14.
2012
|
|
2012
|
Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation..
Thorax.
67:12-18.
2012
|
|
2011
|
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation..
New England Journal of Medicine.
365:1663-1672.
2011
|
|
2011
|
Suppression of CFTR premature termination codons and rescue of CFTR protein and function by the synthetic aminoglycoside NB54..
The Clinical investigator.
89:1149-1161.
2011
|
|
2011
|
Regulatory domain phosphorylation to distinguish the mechanistic basis underlying acute CFTR modulators..
AJP - Lung Cellular and Molecular Physiology.
301:L587-L597.
2011
|
|
2011
|
Quercetin increases cystic fibrosis transmembrane conductance regulator-mediated chloride transport and ciliary beat frequency: therapeutic implications for chronic rhinosinusitis..
American Journal of Rhinology.
25:307-312.
2011
|
|
2011
|
A breath of fresh air..
Scientific American.
305:68-73.
2011
|
|
2011
|
Medicine: A breath of fresh air.
Scientific American.
305:48-53.
2011
|
|
2011
|
Nasal potential difference measurements to assess CFTR ion channel activity..
Methods in Molecular Biology.
741:69-86.
2011
|
|
2010
|
Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation..
New England Journal of Medicine.
363:1991-2003.
2010
|
|
2010
|
Activation of the cystic fibrosis transmembrane conductance regulator by the flavonoid quercetin: potential use as a biomarker of ΔF508 cystic fibrosis transmembrane conductance regulator rescue..
American Journal of Respiratory Cell and Molecular Biology.
43:607-616.
2010
|
|
2010
|
Association of cystic fibrosis genetic modifiers with congenital bilateral absence of the vas deferens..
Fertility and Sterility.
94:2122-2127.
2010
|
|
2010
|
Cystic fibrosis transmembrane conductance regulator protein repair as a therapeutic strategy in cystic fibrosis..
Current Opinion in Pulmonary Medicine.
16:591-597.
2010
|
|
2010
|
A critical role for LTA4H in limiting chronic pulmonary neutrophilic inflammation..
Science.
330:90-94.
2010
|
|
2010
|
An international randomized multicenter comparison of nasal potential difference techniques..
Chest.
138:919-928.
2010
|
|
2010
|
DeltaF508 CFTR processing correction and activity in polarized airway and non-airway cell monolayers..
Pulmonary Pharmacology and Therapeutics.
23:268-278.
2010
|
|
2010
|
Proline-Glycine-Proline (PGP) and High Mobility Group Box Protein-1 (HMGB1): Potential Mediators of Cystic Fibrosis Airway Inflammation..
Open Respiratory Medicine Journal.
4:32-38.
2010
|
|
2010
|
Extensive pulmonary laceration in pediatric trauma..
Respiration.
79:76.
2010
|
|
2009
|
Pharmaceuticals targeting nonsense mutations in genetic diseases: progress in development..
Clinical immunotherapeutics.
23:165-174.
2009
|
|
2008
|
Authors' response.
Thorax.
63:1026.
2008
|
|
2008
|
Potential role of high-mobility group box 1 in cystic fibrosis airway disease..
American Journal of Respiratory and Critical Care Medicine.
178:822-831.
2008
|
|
2008
|
Genetic and reproductive knowledge among adolescents and adults with cystic fibrosis..
Chest.
133:1533.
2008
|
|
2008
|
A novel proteolytic cascade generates an extracellular matrix-derived chemoattractant in chronic neutrophilic inflammation..
Journal of Immunology.
180:5662-5669.
2008
|
|
2008
|
Use of beta blockers and the risk of death in hospitalised patients with acute exacerbations of COPD..
Thorax.
63:301-305.
2008
|
|
2008
|
Authors' response.
Thorax.
63:1027.
2008
|
|
2007
|
Bioelectric effects of quinine on polarized airway epithelial cells..
Journal of Cystic Fibrosis.
6:351-359.
2007
|
|
2007
|
Pulmonary aneurysms and intracardiac thrombi due to Behçet's disease in an African-American adolescent with oculocutaneous albinism..
Clinical Rheumatology.
26:1537-1539.
2007
|
|
2007
|
Restoration of W1282X CFTR activity by enhanced expression..
American Journal of Respiratory Cell and Molecular Biology.
37:347-356.
2007
|
|
2007
|
Detection of cystic fibrosis transmembrane conductance regulator activity in early-phase clinical trials..
Proceedings of the American Thoracic Society.
4:387-398.
2007
|
|
2007
|
No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations..
American Journal of Respiratory Cell and Molecular Biology.
37:57-66.
2007
|
|
2006
|
Advances in cystic fibrosis therapies..
Current Opinion in Pediatrics.
18:604-613.
2006
|
|
2005
|
Cystic fibrosis.
New England Journal of Medicine.
352:2039.
2005
|
|
2005
|
Cystic fibrosis..
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