The utility of cortical-sparing adrenalectomy in pheochromocytomas associated with genetic syndromes

Academic Article

Abstract

  • Management of pediatric patients with pheochromocytomas associated with genetic syndromes, such as Von Hippel-Lindau (VHL) disease, is complex owing to the need for continuous surveillance, high rates of recurrence, multiple operations during childhood, and the possibility of lifelong exogenous steroid replacement. We report the successful treatment of two siblings with VHL who underwent a total of six cortical-sparing procedures without requiring steroid therapy. © 2013 Elsevier Inc.
  • Authors

    Published In

    Digital Object Identifier (doi)

    Author List

  • Fallon SC; Feig D; Lopez ME; Brandt ML
  • Start Page

  • 1422
  • End Page

  • 1425
  • Volume

  • 48
  • Issue

  • 6