Development of profound Chiari I malformation and cerebellar tissue loss and resolution following shunting of posterior fossa extra-axial cyst. Case report.

Academic Article


  • INTRODUCTION: Chiari I malformation can be due to a multitude of etiologies such as craniosynostosis or hydrocephalus. A posterior fossa extra-axial cyst (PFEAC) appears to be an extremely rare cause of this form of hindbrain herniation. CASE REPORT: Herein, we report a case of PFEAC that presented with no Chiari I malformation and then presented months later with a significant Chiari I malformation. Following shunt placement of a PFEAC, striking reversal of the Chiari malformation as well as reconstitution of the cerebellum was noted. CONCLUSIONS: Patients with PFEAC might develop a Chiari I malformation and this might be treated with shunting of the PFEAC alone.
  • Authors

    Published In


  • Hindbrain herniation, Posterior fossa CSF collection, Surgery, Tonsillar ectopia, Treatment, Arnold-Chiari Malformation, Brain Diseases, Cerebellum, Cerebrospinal Fluid Shunts, Child, Preschool, Cranial Fossa, Posterior, Cysts, Female, Humans, Hydrocephalus
  • Digital Object Identifier (doi)

    Pubmed Id

  • 16134564
  • Author List

  • Khan R; Oakes P; Tubbs RS; Oakes WJ
  • Start Page

  • 183
  • End Page

  • 185
  • Volume

  • 33
  • Issue

  • 1