Two cases of an uncommon fundus disorder, pigmented paravenous retinochoroidal atrophy, were presented. Clinical findings to support the diagnosis are pigment cuffs about the larger retinal veins and their bifurcations, surrounding retinochoroidal atrophy of varying degrees, and peripapillary atrophy. Most cases are discovered during routine ophthalmoscopy in patients who are typically asymptomatic. The clinical course of this disorder appears to remain stable or to be slowly progressive. Patients with pigmented paravenous retinochoroidal atrophy rarely, if ever, suffer any significant visual impairment. The previous literature was extensively reviewed, and the differential diagnosis and management of the disorder were described.
